Long-term follow-up of basal cell nevus syndrome

Abstract

The basal cell nevus syndrome is an autosomal dominant disorder, characterized by basal cell carcinomas, odontogenic keratocysts, palmar and plantar pits and ectopic calcification. We experienced a case of 14-year-old girl with three odontogenic keratocysts, bifid rib, and ectopic calcification of falx cerebri. Odontogenic keratocyst recurred two times at about 1 year and 5 months, and about 3 years 1 month after cysts removal. And 4 years and 7 months after first operation, newly forming cyst was developed.